DeCS Server - List Exact Term

Search on:	OLIVOPONTOCEREBELLAR ATROPHIES
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DeCS

Descriptor English:

Olivopontocerebellar Atrophies

Descriptor Spanish:

Atrofias Olivopontocerebelosas

Descriptor Portuguese:

Atrofias Olivopontocerebelares

Synonyms English:

Dejerine-Thomas Syndrome
Olivopontocerebellar Atrophy, Idiopathic

Tree Number:

Definition English:

A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)

Indexing Annotation English:

DF: OPCA

See Related English:

History Note English:

2000(1987)

Allowable Qualifiers English:

Record Number:

19275

Unique Identifier:

D009849

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